Resumo

BUSTAMANTE CABRERA, Gladys  e  QUELCA APAZA, Marisol. SINDROME DE PRUNE BELLY. Rev. Act. Clin. Med [online]. 2014, vol.46, pp. 2447-2451. ISSN 2304-3768.

Prune Belly syndrome is a disease whose etiology is still unknown and is characterized by a triad consisting of agenesis of abdominal muscles, cryptorchidism and dilatation of the urinary tract, also being associated with respiratory and musculoskeletal system malformations. This rare syndrome is present in newborn and infant males, with a frequency of 1 in every 29,000, only 5% occur in females. The clinical manifestations of the triad of abnormalities present in this state, ranging from muscle defect present in the abdominal wall, which consists only of skin and peritoneum, skin tissue which presents a series of striations, which permit easy probing viscera also associating an alteration of the urogenital system characterized by dilation of the bladder as a result of obstruction distal with vesicoureteral reflux.

Palavras-chave : Prune Belly Syndrome; Vesico urethral reflux; Eagle Barret syndrome.